HMBS Antikörper
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- Target Alle HMBS Antikörper anzeigen
- HMBS (Hydroxymethylbilane Synthase (HMBS))
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Reaktivität
- Human, Maus, Ratte
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Wirt
- Kaninchen
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Klonalität
- Polyklonal
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Konjugat
- Dieser HMBS Antikörper ist unkonjugiert
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Applikation
- Western Blotting (WB), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Kreuzreaktivität
- Human, Maus, Ratte
- Aufreinigung
- Purified by Protein A.
- Immunogen
- KLH conjugated synthetic peptide derived from human HMBS/PBGD
- Isotyp
- IgG
- Top Product
- Discover our top product HMBS Primärantikörper
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anti-Hydroxymethylbilane Synthase (HMBS) (AA 283-330) antibody
HMBS Reaktivität: Human WB, ELISA, IHC, IF Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS Reaktivität: Human WB, IF Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS Reaktivität: Human WB, ELISA Wirt: Maus Monoclonal 3E8 unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 85-337) antibodyHMBS Reaktivität: Human WB, IHC, IP, ICC Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (Internal Region) antibodyHMBS Reaktivität: Human, Maus, Ratte WB, ELISA, IHC, IF, ICC Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibodyHMBS Reaktivität: Human WB Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 160-173) antibodyVerified HMBS Reaktivität: Human WB, ELISA, IHC Wirt: Ziege Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) antibodyHMBS Reaktivität: Human, Maus, Ratte WB, ELISA Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (AA 146-195) antibodyHMBS Reaktivität: Human, Kaninchen, Meerschweinchen, Affe WB Wirt: Kaninchen Polyclonal unconjugated
anti-Hydroxymethylbilane Synthase (HMBS) (N-Term) antibodyHMBS Reaktivität: Human, Maus, Ratte, Kaninchen, Hund, Pferd, Meerschweinchen, Rind (Kuh), Zebrafisch (Danio rerio), Schwein, Affe, Fledermaus, Xenopus laevis WB Wirt: Kaninchen Polyclonal unconjugated
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- Applikationshinweise
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WB 1:300-5000
IHC-P 1:200-400
IF(IHC-P) 1:50-200 - Beschränkungen
- Nur für Forschungszwecke einsetzbar
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- Format
- Liquid
- Konzentration
- 1 μg/μL
- Buffer
- 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
- Konservierungsmittel
- ProClin
- Vorsichtsmaßnahmen
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- Lagerung
- 4 °C,-20 °C
- Informationen zur Lagerung
- Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
- Haltbarkeit
- 12 months
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- Target
- HMBS (Hydroxymethylbilane Synthase (HMBS))
- Andere Bezeichnung
- HMBS (HMBS Produkte)
- Hintergrund
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Synonyms: HEM3_HUMAN, HMBS, Hydroxymethylbilane synthase, PBG D, PBG-D, PBGD, Porphobilinogen deaminase, Pre uroporphyrinogen synthase, Pre-uroporphyrinogen synthase, UPS, Uroporphyrinogen I synthase, Uroporphyrinogen I synthetase.
Background: PBGD, also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.
- Gen-ID
- 3145
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