MMADHC Antikörper
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- Target Alle MMADHC Antikörper anzeigen
- MMADHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
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Reaktivität
- Human
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Wirt
- Kaninchen
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Klonalität
- Polyklonal
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Konjugat
- Dieser MMADHC Antikörper ist unkonjugiert
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Applikation
- Western Blotting (WB), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Kreuzreaktivität
- Human
- Aufreinigung
- Purified by Protein A.
- Immunogen
- KLH conjugated synthetic peptide derived from human C2ORF25
- Isotyp
- IgG
- Top Product
- Discover our top product MMADHC Primärantikörper
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- Applikationshinweise
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WB 1:300-5000
IHC-P 1:200-400
IF(IHC-P) 1:50-200 - Beschränkungen
- Nur für Forschungszwecke einsetzbar
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- Format
- Liquid
- Konzentration
- 1 μg/μL
- Buffer
- 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
- Konservierungsmittel
- ProClin
- Vorsichtsmaßnahmen
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- Lagerung
- 4 °C,-20 °C
- Informationen zur Lagerung
- Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
- Haltbarkeit
- 12 months
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- Target
- MMADHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
- Andere Bezeichnung
- C2ORF25 (MMADHC Produkte)
- Synonyme
- C2orf25 antikoerper, CL25022 antikoerper, cblD antikoerper, 2010311D03Rik antikoerper, AI314967 antikoerper, RGD1303272 antikoerper, methylmalonic aciduria and homocystinuria, cblD type antikoerper, methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria antikoerper, MMADHC antikoerper, Mmadhc antikoerper
- Hintergrund
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Synonyms: cblD, Chromosome 2 open reading frame 25, Protein C2orf25, mitochondrial, CL25022, Methylmalonic aciduria cobalamin deficiency cblD type, with homocystinuria, Protein C2orf25, mitochondrial, MMAD_HUMAN.
Background: C2ORF25 is a mitochondrial protein and its function is not fully identified. But, Vitamin B12 (cobalamin) is an essential cofactor in several metabolic pathways. Intracellular conversion of cobalamin to adenosylcobalamin in mitochondria and to methylcobalamin in cytoplasm is necessary for homeostasis of methylmalonic acid and homocysteine. C2ORF25 encodes a protein involved in an early step of cobalamin metabolism.
- Gen-ID
- 27249
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