MCCC2 Antikörper (AA 1-563)
MCCC2
Reaktivität: Human
WB, IF
Wirt: Maus
Polyclonal
unconjugated
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Target
Alle MCCC2 Antikörper anzeigen
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MCCC2
(Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
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Bindungsspezifität
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AA 1-563
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Reaktivität
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Human
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Wirt
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Maus
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Klonalität
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Polyklonal
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Konjugat
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Dieser MCCC2 Antikörper ist unkonjugiert
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Applikation
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Western Blotting (WB), Immunofluorescence (IF)
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Verwendungszweck
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Mouse polyclonal antibody raised against a full-length human MCCC2 protein.
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Sequenz
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MWAVLRLALR PCARASPAGP RAYHGDSVAS LGTQPDLGSA LYQENYKQMK ALVNQLHERV EHIKLGGGEK ARALHISRGK LLPRERIDNL IDPGSPFLEL SQFAGYQLYD NEEVPGGGII TGIGRVSGVE CMIIANDATV KGGAYYPVTV KKQLRAQEIA MQNRLPCIYL VDSGGAYLPR QADVFPDRDH FGRTFYNQAI MSSKNIAQIA VVMGSCTAGG AYVPAMADEN IIVRKQGTIF LAGPPLVKAA TGEEVSAEDL GGADLHCRKS GVSDHWALDD HHALHLTRKV VRNLNYQKKL DVTIEPSEEP LFPADELYGI VGANLKRSFD VREVIARIVD GSRFTEFKAF YGDTLVTGFA RIFGYPVGIV GNNGVLFSES AKKGTHFVQL CCQRNIPLLF LQNITGFMVG REYEAEGIAK DGAKMVAAVA CAQVPKITLI IGGSYGAGNY GMCGRAYSPR FLYIWPNARI SVMGGEQAAN VLATITKDQR AREGKQFSSA DEAALKEPII KKFEEEGNPY YSSARVWDDG IIDPADTRLV LGLSFSAALN APIEKTDFGI FRM
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Kreuzreaktivität
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Human
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Produktmerkmale
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Antibody reactive against mammalian transfected lysate.
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Immunogen
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MCCC2 (NP_071415.1, 1 a.a. ~ 563 a.a) full-length human protein.
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Applikationshinweise
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Optimal working dilution should be determined by the investigator.
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Beschränkungen
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Nur für Forschungszwecke einsetzbar
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Buffer
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In 1x PBS, pH 7.4
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Handhabung
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Aliquot to avoid repeated freezing and thawing.
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Lagerung
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-20 °C
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Informationen zur Lagerung
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Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
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Grünert, Stucki, Morscher, Suormala, Bürer, Burda, Christensen, Ficicioglu, Herwig, Kölker, Möslinger, Pasquini, Santer, Schwab, Wilcken, Fowler, Yue, Baumgartner: "3-methylcrotonyl-CoA carboxylase deficiency: clinical, biochemical, enzymatic and molecular studies in 88 individuals." in: Orphanet journal of rare diseases, Vol. 7, pp. 31, (2012) (PubMed).
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Target
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MCCC2
(Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
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Andere Bezeichnung
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MCCC2 (MCCC2 Produkte)
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Hintergrund
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Full Gene Name: methylcrotonoyl-Coenzyme A carboxylase 2 (beta)
Synonyms: MCCB
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Gen-ID
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64087
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NCBI Accession
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NM_022132
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