Dysferlin Antikörper (C-Term)
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- Target Alle Dysferlin (DYSF) Antikörper anzeigen
- Dysferlin (DYSF)
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Bindungsspezifität
- C-Term
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Reaktivität
- Human
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Wirt
- Kaninchen
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Klonalität
- Polyklonal
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Konjugat
- Dieser Dysferlin Antikörper ist unkonjugiert
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Applikation
- Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Spezifität
- This antibody reacts to Dysferlin, Limb Girdle Muscular Dystrophy 2b (AUTOSOMAL RECESSIVE) (DYSF).
- Aufreinigung
- Immunoaffinity Chromatography
- Immunogen
- A synthetic peptide corresponding to C-terminal of human Dysferlin Genename: DYSF
- Isotyp
- IgG
- Top Product
- Discover our top product DYSF Primärantikörper
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- Applikationshinweise
- Optimal working dilution should be determined by the investigator.
- Beschränkungen
- Nur für Forschungszwecke einsetzbar
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- Buffer
- 10 mM PBS, pH 7.4 containing BSA as stabilizer and 0,09 % sodium azide as preservative
- Konservierungsmittel
- Sodium azide
- Vorsichtsmaßnahmen
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Lagerung
- 4 °C
- Informationen zur Lagerung
- Store the antibody undiluted at 2-8 °C. DO NOT FREEZE!
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- Target
- Dysferlin (DYSF)
- Andere Bezeichnung
- Dysferlin (DYSF Produkte)
- Synonyme
- DYSF antikoerper, fb73b05 antikoerper, wu:fb73b05 antikoerper, si:rp71-50c18.1 antikoerper, DKFZp459E1226 antikoerper, 2310004N10Rik antikoerper, AI604795 antikoerper, D6Pas3 antikoerper, mFLJ00175 antikoerper, FER1L1 antikoerper, LGMD2B antikoerper, MMD1 antikoerper, dysferlin antikoerper, dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive) antikoerper, myoferlin antikoerper, DYSF antikoerper, dysf antikoerper, LOC589501 antikoerper, Dysf antikoerper
- Hintergrund
- Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.Synonyms: DYSF, Dystrophy-associated fer-1-like protein, FER1L1, Fer-1-like protein 1
- Gen-ID
- 8291
- NCBI Accession
- NP_001123927
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