TIMM8A/DDP Antikörper (AA 1-97)

Produktnummer ABIN6149172

Produktdetails anti-TIMM8A/DDP Antikörper

Target: TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))

Bindungsspezifität: AA 1-97

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser TIMM8A/DDP Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: MDSSSSSSAA GLGAVDPQLQ HFIEVETQKQ RFQQLVHQMT ELCWEKCMDK PGPKLDSRAE ACFVNCVERF IDTSQFILNR LEQTQKSKPV FSESLSD

Kreuzreaktivität: Human, Maus

Produktmerkmale: Polyclonal Antibodies

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 1-97 of human TIMM8A (NP_004076.1).

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: WB,1:500 - 1:2000

Kommentare:

HIGH QUALITY

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Avoid freeze / thaw cycles.

Details zu TIMM8A/DDP

Target: TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))

Andere Bezeichnung: TIMM8A (TIMM8A Produkte)

Synonyme: TIMM8A antikoerper, ddp antikoerper, tim8a antikoerper, timm8a antikoerper, DDP antikoerper, DDP1 antikoerper, DFN1 antikoerper, MTS antikoerper, TIM8 antikoerper, im:6896085 antikoerper, zgc:100916 antikoerper, Ddp1 antikoerper, Timm8a antikoerper, DXHXS1274E antikoerper, Fci-12 antikoerper, Tim8a antikoerper, translocase of inner mitochondrial membrane 8 homolog A (yeast) antikoerper, translocase of inner mitochondrial membrane 8A antikoerper, translocase of inner mitochondrial membrane 8 homolog A1 (yeast) antikoerper, translocase of inner mitochondrial membrane 8A1 antikoerper, TIMM8A antikoerper, timm8a antikoerper, Timm8a1 antikoerper

Hintergrund: This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.,TIMM8A,DDP,DDP1,DFN1,MTS,TIM8,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Neuroscience,Neurodegenerative Diseases,TIMM8A

Molekulargewicht: 10 kDa

Gen-ID: 1678

UniProt: O60220