HADHA Antikörper
-
- Target Alle HADHA Antikörper anzeigen
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
-
Reaktivität
- Human, Maus
-
Wirt
- Kaninchen
-
Klonalität
- Polyklonal
-
Konjugat
- Dieser HADHA Antikörper ist unkonjugiert
-
Applikation
- Western Blotting (WB), Immunofluorescence (IF)
- Aufreinigung
- Affinity purification
- Immunogen
- Recombinant protein of human HADHA
- Isotyp
- IgG
- Top Product
- Discover our top product HADHA Primärantikörper
-
-
- Applikationshinweise
- WB 1:500 - 1:2000 IF 1:50 - 1:200
- Beschränkungen
- Nur für Forschungszwecke einsetzbar
-
- Konzentration
- 1 mg/mL
- Buffer
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- Konservierungsmittel
- Sodium azide
- Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Lagerung
- -20 °C
- Informationen zur Lagerung
- Store at -20°C. Avoid freeze / thaw cycles.
-
- Target
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
- Andere Bezeichnung
- HADHA (HADHA Produkte)
- Synonyme
- cb1055 antikoerper, hadha antikoerper, im:7136067 antikoerper, wu:fa14c08 antikoerper, ECHA antikoerper, GBP antikoerper, HADH antikoerper, LCEH antikoerper, LCHAD antikoerper, MTPA antikoerper, TP-ALPHA antikoerper, RGD1560655 antikoerper, C77020 antikoerper, Mtpa antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antikoerper, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antikoerper, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antikoerper, HADHA antikoerper, hadha antikoerper, hadha.S antikoerper, hadhaa antikoerper, Hadha antikoerper
- Hintergrund
-
Synonyms: 3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit,3 oxoacyl CoA thiolase,78 kDa gastrin binding protein,78 kDa gastrin-binding protein,ECHA,ECHA,GBP,HADH,HADHA,Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit,LCEH,LCHAD,Long chain 3-hydroxyacyl-CoA dehydrogenase,Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit,Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit,Mitochondrial trifunctional enzyme alpha subunit,Mitochondrial trifunctional protein alpha subunit,MTPA,Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit,TP ALPHA,TP-alpha,Trifunctional enzyme subunit alpha mitochondrial precursor
Background: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
- Molekulargewicht
-
Observed_MW: 82kDa
Calculated_MW: 28kDa/83kDa
- Gen-ID
- 3030
- UniProt
- P40939
- Pathways
- Monocarboxylic Acid Catabolic Process
-