GLA Antikörper (AA 101-200)

Produktnummer ABIN872875

Produktdetails anti-GLA Antikörper

Target: GLA (Galactosidase, alpha (GLA))

Bindungsspezifität: AA 101-200

Reaktivität: Human, Maus, Ratte

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser GLA Antikörper ist unkonjugiert

Applikation: Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Frozen Sections) (IHC (fro))

Kreuzreaktivität: Human, Maus, Ratte

Homologie: Dog,Cow,Pig,Rabbit

Aufreinigung: Purified by Protein A.

Immunogen: KLH conjugated synthetic peptide derived from human Galactosidase alpha

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: WB 1:300-5000
ELISA 1:500-1000
FCM 1:20-100
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 μg/μL

Buffer: 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.

Konservierungsmittel: ProClin

Vorsichtsmaßnahmen: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Lagerung: 4 °C,-20 °C

Informationen zur Lagerung: Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.

Haltbarkeit: 12 months

Details zu GLA

Target: GLA (Galactosidase, alpha (GLA))

Andere Bezeichnung: Galactosidase alpha (GLA Produkte)

Synonyme: GALA antikoerper, Ags antikoerper, zgc:101584 antikoerper, MGC130872 antikoerper, SMU.877 antikoerper, SCF11.21 antikoerper, AO090005000217 antikoerper, alpha-GAL antikoerper, galactosidase alpha antikoerper, galactosidase, alpha antikoerper, galactosidase alpha S homeolog antikoerper, alpha-galactosidase antikoerper, aga antikoerper, alpha-galactosidase A antikoerper, GLA antikoerper, Gla antikoerper, gla antikoerper, gla.S antikoerper, agaN antikoerper, aga antikoerper, agaL antikoerper, SCO0541 antikoerper, rafA antikoerper, melA antikoerper, galA antikoerper, ANI_1_2528074 antikoerper, ANI_1_1502124 antikoerper, AOR_1_390174 antikoerper, CpipJ_CPIJ002066 antikoerper, MCYG_00962 antikoerper, MCYG_00791 antikoerper, Tsp_02909 antikoerper, Tsp_02508 antikoerper

Hintergrund:

Synonyms: GALA, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Melibiase, GLA

Background: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

Gen-ID: 2717

UniProt: P06280

Pathways: SARS-CoV-2 Protein Interaktom