GBE1 Produkte
(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
Kategorien
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008].
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Ausgewählte GBE1 Kategorien
GBE1 Antikörper
High quality antibodies with extensive validation data.
GBE1 ELISA Kits
Reliable ELISA kits for a wide range of species.
GBE1 Proteine
Proteins for various applications incl. WB, ELISA, IF etc.
Empfohlene GBE1 Antikörper
Produkt
Reaktivität
Applikation
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Applikation
WB, IHC, IP, FACS, IHC (p)
Validierungen
- (9)
Kat. Nr.
ABIN1498396
Menge
100 μL
Datenblatt
Datenblatt
Reaktivität
Human
Applikation
WB, IF, IP, FACS
Validierungen
- (4)
Kat. Nr.
ABIN1498395
Menge
100 μL
Datenblatt
Datenblatt
Reaktivität
Human, Mouse
Applikation
WB, IF
Validierungen
- (3)
Kat. Nr.
ABIN653459
Menge
400 μL
Datenblatt
Datenblatt
Empfohlene GBE1 ELISA Kits
Produkt
Reaktivität
Analytical Method
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Analytical Method
Quantitative Competition ELISA
Validierungen
Kat. Nr.
ABIN1742631
Menge
96 tests
Datenblatt
Datenblatt
Reaktivität
Sheep
Analytical Method
Validierungen
Kat. Nr.
ABIN1773535
Menge
96 tests
Datenblatt
Datenblatt
Reaktivität
Pig
Analytical Method
Validierungen
Kat. Nr.
ABIN1749960
Menge
96 tests
Datenblatt
Datenblatt
Empfohlene GBE1 Proteine
Produkt
Reaktivität
Source
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Source
Wheat germ
Validierungen
- (1)
Kat. Nr.
ABIN1354871
Menge
10 μg
Datenblatt
Datenblatt
Reaktivität
Human
Source
Wheat germ
Validierungen
- (1)
Kat. Nr.
ABIN1354873
Menge
10 μg
Datenblatt
Datenblatt
Reaktivität
Human
Source
HEK-293 Cells
Validierungen
- (1)
Kat. Nr.
ABIN2721752
Menge
20 μg
Datenblatt
Datenblatt
Neueste Publikationen zu unseren GBE1 Produkten
: "Adult polyglucosan body disease: clinical and histological heterogeneity of a large Italian family." in: Neuromuscular disorders : NMD, Vol. 25, Issue 5, pp. 423-8, (2015) (PubMed).: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." in: The Journal of biological chemistry, (2015) (PubMed).
: "A novel mouse model that recapitulates adult-onset glycogenosis type 4." in: Human molecular genetics, Vol. 24, Issue 23, pp. 6801-10, (2015) (PubMed).
: "Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase." in: Journal of neurochemistry, Vol. 127, Issue 1, pp. 101-13, (2013) (PubMed).
: "Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV." in: Human molecular genetics, Vol. 20, Issue 22, pp. 4430-9, (2011) (PubMed).
Synonyme und alternative Namen zu GBE1
1,4-alpha-glucan branching protein GlgB (glgB), 1,4-alpha-glucan branching protein (glgB), glycogen branching protein (ECs4277), glycogen branching protein (glgB), glycogen branching enzyme (glgB), 1,4-alpha-glucan-branching protein (SCO7332), glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase (glgB), glycogen branching enzyme (Synpcc7942_1085), glycogen branching enzyme (AZC_4116), glycogen branching enzyme (Sros_8169), glycogen branching enzyme (Despr_0975), 1,4-alpha-glucan branching enzyme 1 (GBE1), glucan (1,4-alpha-), branching enzyme 1 (Gbe1), 1,4-alpha-glucan branching enzyme 1 (Gbe1), 2310045H19Rik, 2810426P10Rik, APBD, D16Ertd536e, GBE, glgBII, GSD4Bezeichner auf Proteinebene für GBE1
- glycogen branching enzyme
- 1,4-alpha-glucan-branching enzyme
- amylo-(1,4 to 1,6) transglucosidase
- amylo-(1,4 to 1,6) transglycosylase
- brancher enzyme
- glycogen-branching enzyme
- glucan (1,4-alpha-), branching enzyme 1 (glycogen branching enzyme, Andersen disease, glycogen storage disease type IV)
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