GLA Produkte
(Galactosidase, alpha (GLA))
Kategorien
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008].
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Ausgewählte GLA Kategorien
GLA Antikörper
High quality antibodies with extensive validation data.
GLA ELISA Kits
Reliable ELISA kits for a wide range of species.
GLA Proteine
Proteins for various applications incl. WB, ELISA, IF etc.
Empfohlene GLA Antikörper
Produkt
Reaktivität
Applikation
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Applikation
WB, IHC, IP, ICC
Validierungen
- (7)
Kat. Nr.
ABIN7431278
Menge
100 μL
Datenblatt
Datenblatt
Reaktivität
Human
Applikation
WB, IHC, IP, ICC
Validierungen
- (6)
Kat. Nr.
ABIN7426817
Menge
100 μL
Datenblatt
Datenblatt
Reaktivität
Human
Applikation
WB, IP, IHC (p)
Validierungen
- (2)
- (5)
Kat. Nr.
ABIN2854962
Menge
100 μL
Datenblatt
Datenblatt
Empfohlene GLA ELISA Kits
Produkt
Reaktivität
Analytical Method
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Analytical Method
Quantitative Sandwich ELISA
Validierungen
- (5)
Kat. Nr.
ABIN6720556
Menge
96 tests
Datenblatt
Datenblatt
Reaktivität
Human
Analytical Method
Quantitative Sandwich ELISA
Validierungen
- (1)
Kat. Nr.
ABIN3199196
Menge
96 tests
Datenblatt
Datenblatt
Reaktivität
Mouse
Analytical Method
Quantitative Sandwich ELISA
Validierungen
Kat. Nr.
ABIN6730640
Menge
96 tests
Datenblatt
Datenblatt
Empfohlene GLA Proteine
Produkt
Reaktivität
Source
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität
Human
Source
Wheat germ
Validierungen
- (1)
- (1)
Kat. Nr.
ABIN1355176
Menge
10 μg
Datenblatt
Datenblatt
Reaktivität
Human
Source
Escherichia coli (E. coli)
Validierungen
- (1)
Kat. Nr.
ABIN7123037
Menge
50 μg
Datenblatt
Datenblatt
Reaktivität
Mouse
Source
HEK-293 Cells
Validierungen
- (1)
Kat. Nr.
ABIN7320092
Menge
50 μg
Datenblatt
Datenblatt
Neueste Publikationen zu unseren GLA Produkten
: "Rapid Clathrin-Mediated Uptake of Recombinant α-Gal-A to Lysosome Activates Autophagy." in: Biomolecules, Vol. 10, Issue 6, (2020) (PubMed).: "Ligand-promoted protein folding by biased kinetic partitioning." in: Nature chemical biology, Vol. 13, Issue 4, pp. 369-371, (2017) (PubMed).
: "Comparison of intracellular and secretion-based strategies for production of human ?-galactosidase A in the filamentous fungus Trichoderma reesei." in: BMC biotechnology, Vol. 14, pp. 91, (2015) (PubMed).
: "Coformulation of a Novel Human α-Galactosidase A With the Pharmacological Chaperone AT1001 Leads to Improved Substrate Reduction in Fabry Mice. ..." in: Molecular therapy : the journal of the American Society of Gene Therapy, Vol. 23, Issue 7, pp. 1169-81, (2015) (PubMed).
: "Establishing 3-nitrotyrosine as a biomarker for the vasculopathy of Fabry disease." in: Kidney international, Vol. 86, Issue 1, pp. 58-66, (2014) (PubMed).
: "A thermodynamic assay to test pharmacological chaperones for Fabry disease." in: Biochimica et biophysica acta, Vol. 1840, Issue 3, pp. 1214-24, (2014) (PubMed).
: "Integrated approach to produce a recombinant, His-tagged human ?-galactosidase A in mammalian cells." in: Biotechnology progress, Vol. 27, Issue 5, pp. 1206-17, (2011) (PubMed).
: "Protein translocation: how Hsp70 pulls it off." in: Cell, Vol. 97, Issue 6, pp. 679-82, (1999) (PubMed).
: "The Hsp70 and Hsp60 chaperone machines." in: Cell, Vol. 92, Issue 3, pp. 351-66, (1998) (PubMed).
: "Expression of hsp70 induced in CHO cells by 45.0 degrees C hyperthermia is cell cycle associated and DNA synthesis dependent." in: Cytometry, Vol. 19, Issue 2, pp. 119-25, (1995) (PubMed).
Synonyme und alternative Namen zu GLA
galactosidase alpha (GLA), galactosidase, alpha (Gla), galactosidase, alpha (gla), galactosidase alpha S homeolog (gla.S), galactosidase alpha (gla), alpha-galactosidase (agaN), aga (aga), alpha-galactosidase (agaL), alpha-galactosidase (SCO0541), alpha-galactosidase (rafA), alpha-galactosidase (melA), alpha-galactosidase (galA), alpha-galactosidase A (ANI_1_2528074), alpha-galactosidase A (ANI_1_1502124), alpha-galactosidase A (AOR_1_390174), alpha-galactosidase A (CpipJ_CPIJ002066), alpha-galactosidase (aga), alpha-galactosidase A (MCYG_00962), alpha-galactosidase A (MCYG_00791), alpha-galactosidase (gla), alpha-galactosidase A (Tsp_02909), alpha-galactosidase A (Tsp_02508), galactosidase alpha (Gla), galactosidase, alpha (GLA), Ags, alpha-GAL, AO090005000217, GALA, MGC130872, SCF11.21, SMU.877, zgc:101584Bezeichner auf Proteinebene für GLA
- agalsidase alfa
- alpha-D-galactosidase A
- alpha-D-galactoside galactohydrolase 1
- alpha-gal A
- alpha-galactosidase A
- melibiase
- alpha-D-galactoside galactohydrolase
- Alpha-galactosidase A
- galactosidase, alpha
- alpha-galactosidase A-like
- alpha-galactosidase
- Alpha-galactosidase
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